기저세포모반증후군과 연관된 다발성 치성각화낭종의 치료시 술전 조대술과 술후 교정적 맹출의 사용 치험 1례
Case report of treatment of multiple odontogenic keratocysts with basal cell nevus syndrome using preoperative marsupialization and orthodontic extrusion
강태인, 박영주, 남정훈, 송준호, 안장훈, 정재안, 신진업, 강혜진,
소속 상세정보
강태인 ( Gang Tae-In ) - 한림대학교 의과대학 강남성심병원 구강악안면외과학교실
박영주 ( Park Young-Ju ) - 한림대학교 의과대학 강남성심병원 구강악안면외과학교실
남정훈 ( Nam Jeong-Hun ) - 한림대학교 의과대학 강남성심병원 구강악안면외과학교실
송준호 ( Song Jun-Ho ) - 한림대학교 의과대학 강남성심병원 구강악안면외과학교실
안장훈 ( Ahn Jang-Hoon ) - 한림대학교 의과대학 강남성심병원 구강악안면외과학교실
정재안 ( Chung Jae-An ) - 한림대학교 의과대학 강남성심병원 구강악안면외과학교실
신진업 ( Shin Jin-Eob ) - 한림대학교 의과대학 강남성심병원 구강악안면외과학교실
강혜진 ( Kang Hae-Jin ) - 한림대학교 의과대학 강남성심병원 구강악안면외과학교실
KMID : 0360120090310050429
Abstract
Basal cell nevus syndrome is a rare inherited disorder characterized by mulitple cutaneous basal cell carcinoma, pits of the palms and soles, cysts of the jaws, skeletal abnormalities and ectopic calcifications. Currently there are new lines of investigation based on biomolecular studies, which aim at identifying the molecules responsible for these cysts and thus early allowing an early diagnosis of these patients. We report a case of a 9-year-old boy with the various manifestation of basal cell nevus syndrome, which are multiple odontogenic keratocysts, pits of the soles, bifid ribs, ectopic calcification, macrocephaly, and hypertelorism, etc. Total five odontogenic keratocysts were found. For the reduction of the size of the odon-togenic keratocysts, following preoperative marsupialization, there were surgically enucleated. And the impacted upper right lateral incisor and canine are tracted orthodontically.
키워드
Odontogenic keratocyst;Basal cell nevus syndrome;Marsupialization;Orthodontic extrusion
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